Immunoglobulin G4-related sclerosing cholangitis
Goodchild George, Pereira Stephen P., Webster George,
소속 상세정보
( Goodchild George )
University College Hospital Department of Gastroenterology
( Pereira Stephen P. )
University College Hospital Department of Gastroenterology
( Webster George )
University College Hospital Department of Gastroenterology
Abstract
Immunoglobulin G4-related disease (IgG4-RD) is a systemic fibroinflammatory condition of which IgG4-related sclerosing cholangitis (IgG4-SC) is the biliary manifestation. In this review, we provide an overview of IgG4-RD, with a focus on the biliary manifestations. In particular, we describe the important differential diagnoses of IgG4-SC, namely, primary sclerosing cholangitis and cholangiocarcinoma, outline diagnostic criteria for IgG4-SC, provide insight into possible pathophysiological mechanisms underlying the disease and discuss short and long-term management options of this recently described disease.
키워드
Immunoglobulin G4 related disease; Immunoglobulin G4 cholangiopathy; Autoimmune pancreatitis; Cholangitis, sclerosing; Biliary stricture
원문 및 링크아웃 정보
등재저널 정보
SCI(E)
MEDLINE
KCI
KoreaMed
KAMS