성인에서의 Hirschsprung씨 질환
Hirschsprung’s Disease in Adults and Adolescents
서정길, 김종헌, 황용,
소속 상세정보
서정길 ( Seo Jung-Gil )
전북대학교 의과대학 외과학교실
김종헌 ( Kim Jong-Hun )
전북대학교 의과대학 외과학교실
황용 ( Hwang Yong )
전북대학교 의과대학 외과학교실
KMID : 0356719960120010069
Abstract
Hirschsprung’s disease is a disorder characterized by congenital abscence of ganglion cells in the colon and the rectum variously. Generally, the symptoms of it are present during the first day of the life, and the diagnosis is usually made early. There may be a period of normal defecation for months or years after mild fecal dyskinesia in the neonatal period, and clinicians are occasionally fased with young adults or adults with undiagnosed megacolon or megarectum. In contrast to reports of newborns and young children, there are few rescent reports of the diagnosis and management of Hirschsprung’s disease in adults. We experienced 5 patients over the age of 10 years (11∼59 years) with Hirschsprung’s disease confirmed by full thickness rectal biopsy. 3 males and 2 females were treated by Soave procedure (2), Duhamel procedure(1), lower anterior resection(1) and anorectal myectomy(1), respectively. And we followed up over 1 years(1∼4years). The results of this procedure in the treatment of the adult Hirschsprung’s disease are as good as it of child Hirschsprung’s disease. And we concluded this operative method can be performed to adult Hirschsprung’s disease safely according to cases.
키워드
Hirschsprung’s disease
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