가족성 용종증 수술후 발생한 절제 불가능한 유건종(Desmoid tumor) 1예
Unresectable Desmoid Tumor Developing after Surgery of F.A.P Case report
이현석, 김정수, 김재성, 이은정, 전해명, 오승택,
소속 상세정보
이현석 ( Lee Hyun-Seok )
가톨릭대학교 의과대학 일반외과학교실
김정수 ( Kim Jeong-Soo )
가톨릭대학교 의과대학 외과학교실
김재성 ( Kim Jae-Sung )
가톨릭대학교 의과대학 일반외과학교실
이은정 ( Lee Eun-Jung )
가톨릭대학교 의과대학 임상병리학교실
전해명 ( Jeon Hae-Myung )
가톨릭대학교 의과대학 외과학교실
오승택 ( Oh Seung-Tack )
가톨릭대학교 의과대학 외과학교실
KMID : 0356719980140020323
Abstract
Desmoid tumors are defined as aggressive overgrowth of fibrous sheets and musculoaponeurotic structures. Although desmoid tumors are generally known as a benign neoplasm, it’s aggresive local invasiveness and frequent recurrence indicate it’s position lying between the benign and malignancy. The association of desmoid tumor and familial adenomtous polyposis(FAP) was first made in 1923 by Nichols. In 1951, Gardner reported the familial occurrence of intestinal polyposis, osteomas, fibromas, and epidermal or sebaceous cyst. Desmoid tumors are common in patients with FAP and Occur in 3.5∼29% of patients with FAP whereas the incidence in the gerenal population is 2∼5/1,000,000 person years. Surgical resection of desmoids in patients with FAP has been controversial because unresectability and recurrence are more common than cure. Palliative and curative resections have a high morbidity. Surgery should be reserved for those patients with symptomatic mesenteric desmoids. If a small mesenteric desmoid is encountered incidentally and is easily resectable, it should be resected. If surgery has been less than satisfactory in the treatment of these patients, several different medical approaches can be combined with or without surgical resection with mixed result. Authors report a case of unresectable mesenteric desmoid tumor, developing after surgery of FAP and literatures were reviewed
키워드
Desmoid tumor;F.A.P(Familial adenomatous polyposis)
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