Gardner 증후군 1예-복강내 종괴로 개복 후 확인된 Gaidner증후군 1예-
Gardnerls Syndrome-Report of one case-
오영석, 안병권, 백승언, 이승도,
소속 상세정보
오영석 ( Oh Young-Seok )
고신대학교 복음병원 일반외과
안병권 ( Ahn Byung-Kwon )
고신대학교 복음병원 일반외과
백승언 ( Baek Sung-Uhn )
고신대학교 복음병원 일반외과
이승도 ( Lee Seung-Do )
고신대학교 복음병원 일반외과
KMID : 0356719980140030621
Abstract
Gardner’s syndrome is a familial disease consisting of gastrointestinal adenomatous polyposis, osteomas of the mandible, skull, and long bones, and a variety of sol tissue lesions, including sebaceous cysts, fibromas, lipomas, and desmoid tumors. The colon is the most common site for polyposis, but the stomach, duodenum, small bowel, and periampullary area may also be involved. The diagnostic evaluation, malignant potential, and management is identical to that for familial adenomatous polyposis. The extracolonic manifestations of Gardner’s syndrome are frequent and varied. Gardner’s syndrome is inherited as autosomal dominant traits. Authors experienced one case that is a 32 year old female patient who had colonic and duodenal multiple polyposis, desmoid tumor in abdominal wall and right mesocolon and odontoma on mandible.
키워드
Gardner’s syndrome;Desmoid;Odontoma
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