신경섬유종증 1형에서 발생한 상행결장 장간막 총상형 신경섬유종
Plexiform Neurofibroma Involving the Ascending Colonic Mesentery in Neurofibromatosis Type I
박선진, 이길연, 최성일, 이석환,
소속 상세정보
박선진 ( Park Sun-Jin )
경희대학교 의과대학 외과학교실
이길연 ( Lee Kil-Yeon )
경희대학교 의과대학 외과학교실
최성일 ( Choi Sung-Il )
경희대학교 의과대학 외과학교실
이석환 ( Lee Suk-Hwan )
경희대학교 의과대학 외과학교실
KMID : 0356720090250040259
Abstract
We report a rare case of plexiform neurofibroma involving the ascending colonic mesentery in von Recklinghausen disease. A 20-yr-old male with neurofibromatosis type I was admitted because of abdominal pain, nausea, and vomiting. On physical examination, there were multiple cafe-au-lait spots over the patient’s entire body. An abdominal computed tomography scan showed a hypodense mass in the ascending colonic mesentery. He underwent a laparoscopic right hemicolectomy with complete excision of the mass. The histological examination showed that the mass consisted of wavy, long-spindled cells, and the immunohistochemical stain for S-100 protein confirmed the mass to be a neurofibroma of the mesentery. The patient had an uneventful postoperative course and no signs of recurrence 16 mo after operation.
키워드
신경섬유종증 1형;총상형 신경섬유종;장간막
von Recklinghausen disease;Plexiform neurofibroma;Mesentery
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