난소에 발생한 Sek Cord Tumor with Annular Tubules-1례보고 및 문헌고전-
Sex Cord Tumor with Annular Tubules-A Case report with review of the literature-
박무균, 곽현숙, 윤주홍, 최건,
소속 상세정보
박무균 ( )
고려대학교 의과대학 임상병리학교실
곽현숙 ( )
고려대학교 의과대학 임상병리학교실
윤주홍 ( )
고려대학교 의과대학 임상병리학교실
최건 ( )
고려대학교 의과대학 임상병리학교실
KMID : 0357919780120030239
Abstract
The rare "sex cord tumor with annular tutules" is commonly multifocal and of
microscopic size and histologically characterized by the presence of simple and complex
annular tubules with hyaline bodies and a tendency to calcification. It is thought to prise
from granulosa cells but to grow in a pattern of Sertoli ceIls. It occurs
disproportionateIy often in patients with Peutz-Jeghers syndrome. In some cases,
estrogenic manifestations are present. There is vigorous histogenic and taxonomic
controversy in ovarian stroma and sex cord origin tumors including sex cord tumor with
annular tubules. It is due in part to a lack of agreement regarding basic embryologic
concepts of gonadogenesis and in part to the potential of genital ridges for
differentiating in either testis or ovary.
Recently authors experienced a case of sex cord tumor with annular tubules in a 11
year old female who revealed precocious breast enlargement and the emergence of pubic
and axillary hairs. The size of the tumor(25×15×15cm) seemed to be the largest among
the reported cases and the histology is identical with Scully's cases. A case report with
review of the literature was performed.
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