Angioimmunoblastic Lymphadenopathy with Dysproteinemia -1예 보고-
Angioimmunoblastic Lymphadenopathy with Dysproteinemia -Report of a Case-
원남희, 정형목, 백승룡,
소속 상세정보
원남희 ( )
고려대학교 의과대학 임상병리과
정형목 ( )
고려대학교 의과대학 임상병리과
백승룡 ( )
고려대학교 의과대학 임상병리과
KMID : 0357919790130020155
Abstract
A new clinico-pathologic disease of Iymphoid system has been reported as immuno-
blastic Iymphadenopathy by Lukes and Tindle and as angioimmunoblastic Iymph-
adenopathy with dysproteinemia (AILD) by Frizzera et. at.
Clinically it occurs most commonly in elder person is characterized by acute onset of
constitutional symptoms, generalized Iymphadenopathy, hepatosplenomegaly and immuno-
logic abnormalitis such as consistent polyclonal gammopathy and often hemolytic anemia.
Histologically it has a diagnostic triad ; 1) loss of nodal architecture and pleomorphic
infiltration of immunoblasts, plasmacytoid immunoblasts, plasma cells and Iymphocytes,
2) prominent proliferation of arborizing small vessels and 3) deposit of PAS-positive
amorphous material in the interstitium.
We report here a case of angioimmunoblastic Iymphadenopathy with dysproteinemia of
a 64 year old male patient and review the literature.
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