매독과 동반된 발작성 한냉 혈새소 뇨증 1예 보고
A Case Report of Paroxysmal Cold Hemoglobinuria Associated with Syphilis
송만수, 맹국영, 김진용, 노흥규,
소속 상세정보
송만수 ( )
충남대학교 의과대학 임상병리학교실
맹국영 ( )
충남대학교 의과대학 임상병리학교실
김진용 ( )
충남대학교 의과대학 임상병리학교실
노흥규 ( )
충남대학교 의과대학 임상병리학교실
KMID : 0357919810150010079
Abstract
One case of rare autoimmune hemolytic syndrome, paroxysmal cold hemoglobinuria
(PCH) is reported.
PCH is one of the rarest of the autoimmune hemolytic syndrome, characterized by
acute intermittent hemolysis, frequently with hemoglobinuria, abdominal pain and periodic
attacks of fever, following local or general exposure to cold, and then a positive
Donath-Landsteiner test, positive Ehrlich reaction test, occasionally positive Rosenbach
test, and/or often associated with syphilis and recent viral infection.
The present case was admitted with chief complaints of headache, dizziness and
occasionally abdominal pain.
According to several : laboratory findings, the case which we have presented here was
thought to be compatible with paroxysmal cold hemoglobinuria associated with syphilis.
The patient appeared to show poor clinical improvement in response to prednisolone in
dose of 30mg per day, blood transfusion and other conservative management.
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