Cyclopia 부검 1예 보고
An Autopsy Case of Cyclopia
이민철, 정형목, 정지용, 임정재,
소속 상세정보
이민철 ( )
고려대학교 의과대학 임상병리과
정형목 ( )
고려대학교 의과대학 임상병리과
정지용 ( )
고려대학교 의과대학 임상병리과
임정재 ( )
서울간호전문대학 부속병원 소아과
KMID : 0357919820160020250
Abstract
The term "cyclos" designates a congenital anomaly of a bilateral symmetrical
malformation of the head in which there is absent or poorly developed median
structures. However, it would be more inclusively defined that anomaly in which the
eyes are closely adjacent as to lie within a single orbit.
The cyclopic monster presented here was still-born from a 28 year-old woman. The
bady was delivered in 33 weeks of gestation and the mother had a history of ingestion
of diagestive drugs during pregnancy. The baby presented the malformation of the head
consisting of single orbital cavity in the midline containing one eyeball with two fused
corneas and one pupil, no nobs nor oral cavity, but synotia. The skull stowed a single
flattened anterior cranial fosse, absence of crista calli and narrow bells turcica. The
brain presented the great degree of malformation in the anterior telencephalon, which
failed to divide into to o hemispheres and was only composed of horseshoe, shaped or
inverted mushroom-like structure.
The third ventricle was greatly dilated and it's roof was bollooned out to form a cyst
filling the greater part of the cranial cavity. The diencephalon was noted as unpaired
protuberence in the floor of malformed forebrain. The pons, medulla and cerebellar
hemisphere were well developed. Olfactory bulges and tracts and left optic nerve were
absent.
키워드
원문 및 링크아웃 정보
등재저널 정보