공뇌증(孔腦症, PORENCEPHALY) -1부검 예 보고-
Porencephaly -An Autopsy Case Report-
소속 상세정보
이효진/Hyo Jin Lee
박문향/박효숙/지제근/Moon Hyang Park/Hyo Sook Park/Je Geun Chi
KMID : 0357919830170030378
Abstract
Porencephaly is a rare congenital anomaly characterized by a cavitary hole extending
from the cerebral mantle to the ventricle of the brain and covered by leptomeningeal
membrane. It is now generally believed that the porencephaly respresents a fetal or
neonatal destructive process of the neural tissue. Authors experienced an autopsy case
of bilateral porencephaly in a 35 day old Korean male infant who died of pneumonia.
The brain weighed 227 ems and morphologically well formed except for two large
symmetric defects at the fronto-pariental region. These defects were characterized by
cleft-like shape, covering the entire cerebral mantle with resultant direct communication
between ventricular cavity and leptomeninges. Thin leptomeningeal trabeculae were
covering the cavity. There was a smooth transition between ependyma and roof of the
defects. No evidence of inflammation or circulatory disturbance was present in the brain.
The remaining central nervous system was unremarkable.
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