요막관기형 - 2증례 보고-
Urachal anomaly -Two Cases Report-
소속 상세정보
김정란/Jung Ran Kim
서은희/지제근/김형수/김충희/Eun Hee Suh/Je Guen Chi/Byung Soo Kim/Choong Hee Kim
KMID : 0357919860200030349
Abstract
Two cases of urachal anomaly (1 urachal cyst and 1 patent urachus) are reported in a
neonate and an eleven year old boy, respectively.
In case 1, the patient was born after an uncomplicated pregnancy to a mother who
had taken progesterone during the first trimester. Because of breech presentation,
cesarian section was elected to deliver a male baby weighing 2.3㎏ who showed
abdominal distension. The patient died of respiratory difficulty several minutes after
birth. At autopsy, there was a large cyst in the midpoint of the abdominal and pelvic
cavity. This round cyst was composed of two components, urachus and urinary bladder.
No area of umbilicocystic fistula was present. The lining epithelium was chiefly of
transitional type.
Associated anomalies were segmental stenosis of posterior urethra, absence of
abdominal musculature, bilateral polycystic kindney of Potter type Ⅳ, hydroureter, and
hypoplasia of lungs. Low set ears, micrognathia and club foot were also present.
In case 2 the patient was 11, year old boy. He had suffered from intermittent urinary
dribbling from untobilicus since early infancy, whenever the abdomiilal pressure was
increased. The patency of urachus was confirmed by fistulography. and the urachal
anomaly was surgically removed. Histopathologically the rejected patent urachus
consisted of pseudostratified columnar to transitional epithelium resting on fibrous
stroma mixed with well formed smooth muscle bundles.
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