단독성 두개내 Rosai-Dorfman병 -1예 보고-
Isolated Intracranial Rosai-Dorfman Disease -A Case Report-
박진규, 조미연, 변진수, 박광하,
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박진규 ( Park Jin-Kyu )
연세대학교 원주의과대학 병리학교실
조미연 ( Cho Mee-Yon )
연세대학교 원주의과대학 병리학교실
변진수 ( Pyen Jhin-Soo )
연세대학교 원주의과대학 신경과학교실
박광하 ( Park Kwang-Hwa )
연세대학교 원주의과대학 병리학교실
KMID : 0357920040380060430
Abstract
Rosai-Dorfman disease (RDD) is an idiopathic histioproliferative disorder of the lymph nodes and extranodal sites. Central nervous system involvement is extremely rare. Intracranial RDD, especially the isolated form, resembles meninigioma both clinically and radiologically. Here, we report a case of isolated, intracranial, dura-based RDD. The patient presented with headache and dizziness with no evidence of lymphadenopathy. Histologically, the lesion consisted of large histiocytes with emperipolesis and lymphoplasma cell infiltrates with a fibrotic background. We discuss the differential diagnosis of this lesion. To our knowledge, this is the first reported Korean case of intracranial RDD.
키워드
Rosai Dorfman disease;Meninges;Intracranial
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