Rosai-Dorfman Disease: Report of a Case Associated with IgG4-Related Sclerotic Lesions
박봉희, Son Da-Hye, 김명환, 심태선, 이희진, 허주령,
소속 상세정보
박봉희 ( Park Bong-Hee )
University of Ulsan College of Medicine Asan Medical Center Department of Pathology
( Son Da-Hye )
University of Ulsan College of Medicine Asan Medical Center Department of Pathology
김명환 ( Kim Myung-Hwan )
University of Ulsan College of Medicine Asan Medical Center Department of Gastroenterology
심태선 ( Shim Tae-Sun )
University of Ulsan College of Medicine Asan Medical Center Department of Pulmonology
이희진 ( Lee Hee-Jin )
University of Ulsan College of Medicine Asan Medical Center Department of Pathology
허주령 ( Huh Joo-Ryung )
University of Ulsan College of Medicine Asan Medical Center Department of Pathology
KMID : 0357920120460060583
Abstract
We describe a rare case of sinus histiocytosis with massive lymphadenopathy (Rosai-Dorfman disease) associated with a six-year history of autoimmune pancreatitis, which was controlled by steroid treatment. The patient presented with multiple, cervical and thoracic lymphadenopathy and abnormal, nodular opacities in the lung. Histologically, Rosai-Dorfman disease with numerous IgG4-positive cells was identified in a subcutaneous lymph node in the patient’s left forearm. The patient recovered uneventfully with steroid treatment.
키워드
Rosai-Dorfman disease; Histiocytosis; sinus; Immunoglobulin G4
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