부신성기 증후군의 1례
A Case of Adrenogenital Syndrome
소속 상세정보
오흥식/Oh HS
KMID : 0358319730140030239
Abstract
The adrenogenital syndrome owing to congenital adrenal hyperplasia is an inborn error of adreno-cortical metabolism, as a result of excessive adrenal androgens. producing heterosexual virlizing changes in females and isosexual precocity in males. Here, a case of adrenogenital syndrome developed in 14 year-old Korean female was presented. She had an enlarged clitoris and vaginal introitus communicated to the urethra interior to the urethral meatal opening at the perineum, resembling perineal hypospadiac penis. Exploration of the pelvic cavity and left adrenal gland revealed normal female internal genital organs and hyperplastic adrenal gland. Constructive operation including vaginoplasty and clitoridectomy was performed.
키워드
부신성기증후군; adrenogenital syndrome
원문 및 링크아웃 정보
등재저널 정보