Immunoglobulin G4-Related Systemic Sclerosing Disease: A Case Involving the Ureter and Kidney
Kim Sun-Chan, 김태구, 최승권, 김명준, 민경은, 이형래, 유구한,
소속 상세정보
( Kim Sun-Chan )
Kyung Hee University Hospital Department of Urology
김태구 ( Kim Tae-Gu )
Kyung Hee University Hospital Department of Urology
최승권 ( Choi Seung-Kwon )
Kyung Hee University Hospital Department of Urology
김명준 ( Kim Myung-Joon )
Kyung Hee University Hospital Department of Urology
민경은 ( Min Gyeong-Eun )
Kyung Hee University Hospital Department of Urology
이형래 ( Lee Hyung-Lae )
Kyung Hee University Hospital Department of Urology
유구한 ( Yoo Koo-Han )
Kyung Hee University Hospital Department of Urology
KMID : 0358320130540030209
Abstract
Immunoglobulin (Ig) G4-related sclerosing disease is a newly defined clinicopathological entity characterized by lymphoplasmacytic infiltration of IgG4-positive plasma cells and varying degrees of fibrosis within affected tissues. Patients usually exhibit multisystem involvement and often respond well to steroid and immunosuppressive therapy. This report presents a case of IgG4-related sclerosing disease involving the ureter and kidney. We hope to bring IgG4-related sclerosing disease to the attention of urologists, because it is an uncommon disease that commonly responds to systemic corticosteroids.
키워드
Immunoglobulin G;Sclerosis;Ureter
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