마미총에 발생한 원시신경외배엽종 - 증례 보고 -
Primitive Neuroectodermal Tumor in the Cauda Equina Region - Case Report -
소속 상세정보
이정만/Jeong Man Lee
이봉암/박종태/임영진/김태성/임언/김국기/Bong Arm Rhee/Jong Tea Park/Young Jin Lim/Tae Sung Kim/Won Leem/Gook Ki Kim
KMID : 0359819990280010123
Abstract
결론
마미총의 원시신경외배엽종은 매우 드문 질환으로 알려져 있다. 최근 저자들은 마미총에
발생한 원시신경외배엽종 1례를 경험하였기에 문헌 고찰과 함께 보고하는 바이다. 매우 악
성이며 국소적 재발을 잘 하기 때문에 수술 및 방사선 치료등 적극적인 치료가 시행되어야
할 것으로 사료된다.
#초록#
We report a malignant peripheral primitive neuroectodermal tumor(PNET) that
originated in the cauda equina in a young adult. After gross total excision of the tumor,
radiotheraphy was followed. The tumor had the typical appearance of a PNET with
small, round cell. It stained positively for the neuron-specific enolase(NSE), conforming
its neural origin and negatively for cytokeratin, glial fibrillary acidic protein(GFAP) and
S-100 protein.
Three months later, MRI showed almost total obstruction at the level of the
L3/L4 interspace caused by a mass occupying the spinal canal
and extending into the L5/S1 foramen on the right. Sixteen
months after commencement of radiotherapy, severe left sciatica developed and MRI
showed involvement of the both and right femur with a large soft tissue mass
extending into the pelvis. Palliative radiotherapy was administered but the patient died
four months later.
키워드
Primitive neuroectodermal tumor(PNET); Cauda equina; Peripheral;
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