선천성 장 중복증의 임상적 특성 및 치료 결과
Clinical Characteristics and Management of Congenital Intestinal Duplication
이상호, 김기홍, 정성은, 이성철, 박귀원, 김우기,
소속 상세정보
이상호 ( Lee Sang-Ho )
서울대학교 의과대학 외과학교실
김기홍 ( Kim Ki-Hong )
서울대학교 의과대학 외과학교실
정성은 ( Jung Sung-Eun )
서울대학교 의과대학 외과학교실
이성철 ( Lee Seong-Cheol )
서울대학교 의과대학 외과학교실
박귀원 ( Park Kwi-Won )
서울대학교 의과대학 외과학교실
김우기 ( Kim Woo-Ki )
서울대학교 의과대학 외과학교실
KMID : 0371320010610050530
Abstract
Purpose : Intestinal duplications are rare congenital malformations that may require surgical intervention. This study attempted to elucidate the clinical characteristics and the management of this disease.
Methods : We reviewed the experience of 13 intestinal duplications confirmed with postoperative pathologic reports from January 1989 to September 2001 at Seoul National University Children’s hospital.
Results : Nine patients were female and 4 were male. Ages ranged from a few days to 5 years (61.4% younger than 1 year). The most common symptom was a vomiting. The major diagnostic method recorded was abdominal ultrasonography. The
location
of
the 12 cystic duplicaions was the ileum in 7 cases, the anus in 2 cases, the duodenun in 1 case, the jejunun in 1 case and the rectum in 1 case. A tubular duplication from the transverse colon to the anus with communication was found in one case.
The
diameter of the cystic duplications averaged 3.45 ㎝, and the average length of the tubular duplication was 40 ㎝. Treatment used was resection and anastomosis of the involved intestine in 8 cases, septostomies in 2, anoplasty in 1,
marsupialization in
1 and transanal excision in 1. There were no postoperative complications or mortality experienced. Gastric mucosa was found in 3 of 7 ileal duplications, small intestinal mucosa was found in the duodenal duplication, and squamous epitheliums were
found
in the rectal and anal duplications.
Conclusion : Congenital intestinal duplication presents as an intestinal obstruction or an abdominal mass in childhood. Abdominal ultrasonography is a major diagnostic method and surgical intervention is mandatory.
키워드
장 중복증; 낭성형; 관성형; Intestinal duplication; Cystic; Tubular;
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