후복막강과 종격동에서 발생한 부신경절종
Paraganglioma Arising from Retroperitoneum, Mediastinum
인승현, 권오정, 박재정, 정파종, 이흥우, 곽진영, 정원상, 이광수, 이경근,
소속 상세정보
인승현 ( In Seung-Hyun )
한양대학교 의과대학 외과학교실
권오정 ( Kwon Oh-Jung )
한양대학교 의과대학 외과학교실
박재정 ( Park Jae-Jeong )
한양대학교 의과대학 외과학교실
정파종 ( Jung Pa-Jong )
한양대학교 의과대학 외과학교실
이흥우 ( Lee Heung-Woo )
한양대학교 의과대학 외과학교실
곽진영 ( Kwak Jin-Young )
한양대학교 의과대학 외과학교실
정원상 ( Chung Won-Sang )
한양대학교 의과대학 흉부외과학교실
이광수 ( Lee Kwong-Soo )
한양대학교 의과대학 외과학교실
이경근 ( Lee Kyeong-Geun )
한양대학교 의과대학 외과학교실
KMID : 0371320010610060619
Abstract
A paraganglioma that arises from the Retroperitoneum, mediastinum is an extra-adrenal form of pheochromcytoma. Extra-adrenal pheochromocytomas can occur at any site in the abdomen where chromaffin tissue is located and have been found in the
paravertebral ganglia, the organ of Zuckerkandl, and the urinary bladder. An extra-adrenal pheochromocytomas can arise from a collection of para-aortic, paraganglion cells located at the origin of the inferior mesenteric artery, This collection
of
paraganglia was first described in fetuses by Zuckerkandl in 1901 and has subsequently been referred to as the organ of Zuckerkandl. Extra-adrenal pheochromocytoma generally secrete norepinephrine, not epinephrine, because there is an absence of
the
enzyme phenyl- ethanolamine-N-methyl transferase. Therefore symptoms are related to the production of norepinephrine. Extra-adrenal pheochromocytomas pursue a more aggressive course than their adrenal counterparts. It was found to metastasize in
approximately 20% to 40% of cases, compared with only a 2% to 10% rate of metastasis in all adrenal tumors. We report on a three case of paragangliomas that had a functional and non-functional paraganglioma of the organ of Zuckerkandl and a case
of
a
non-functional paraganglioma of the posterior mediastinum.
키워드
부신경절; Zuckerkandl 기관; Paraganglioma; Organ of Zuckerkandl;
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