원발성 후복막 활막 육종
A Case of Primary Retroperitoneal Synovial Sarcoma
손보성, 구영미, 유승진, 김기환, 김정수, 안창혁, 이은정, 김욱, 임근우,
소속 상세정보
손보성 ( Sohn Bo-Sung )
가톨릭대학교 의과대학 의정부성모병원 외과학교실
구영미 ( Ku Young-Mi )
가톨릭대학교 의과대학 의정부성모병원 방사선학교실
유승진 ( Yoo Seong-Jin )
가톨릭대학교 의과대학 의정부성모병원 외과학교실
김기환 ( Kim Kee-Hwan )
가톨릭대학교 의과대학 의정부성모병원 외과학교실
김정수 ( Kim Jeong-Soo )
가톨릭대학교 의과대학 의정부성모병원 외과학교실
안창혁 ( An Chang-Hyeok )
가톨릭대학교 의과대학 의정부성모병원 외과학교실
이은정 ( Lee Eun-Jung )
가톨릭대학교 의과대학 의정부성모병원 임상병리학교실
김욱 ( Kim Wook )
가톨릭대학교 의과대학 의정부성모병원 외과학교실
임근우 ( Lim Keun-Woo )
가톨릭대학교 의과대학 의정부성모병원 외과학교실
KMID : 0371320030640030256
Abstract
A retroperitoneal Synovial Sarcoma is defined as a tumor arising in the retroperitoneal space, with an origin of mesodermal structures. The majority of synovial sarcomas (85 to 95%) occur in the extremities, located near the large joints. They are uncommon, and usually appear as a non-specific soft tissue mass, with no specific imaging feature. However, in some cases, radiological findings and anatomic location of the tumor may help the diagnosis. On CT examination, these tumors may be shown as hypo-dense masses and have an irregular enhancement in the periphery, with a poor enhancement in the central area, reflecting the necrotic, cystic and hemorrhagic changes. Histologically, there are two types of synovial sarcoma: biphasic and monophasic. Both types have about a 40% mortality rate. The known prognostic factors are; frequent mitotic figures, extensive tumor necrosis, and poor differentiation. Surgical ablation remains the mainstay of their management. Regardless of adequate surgical and adjunctive therapies, the recurrence rate ranges from 28 to 36%. Here, we present a case of a retroperitoneal synovial sarcoma, with a review of the literature.
키워드
후복막 신생물;활막육종
Retroperitoneal neoplasm;Synovial sarcoma
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