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A Case of Acute Necrotizing Encephalopathy
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±èÀÚÇü/Ja Hyung Kim
À±ÇýÁø/±è´ö¼ö/°íżº/ÃÖÃæ°ï/Hye Jin Yun/Deok Soo Kim/Tae Sung Ko/Choong Gon Choi
KMID : 0391520010090010134
Abstract
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Acute necrotizing encephalopathy is a recently established disease entity, proposed by Mizuguchi et al in 1995, that shows a characteristic symmetric and multifocal involvement of both thalamus, brainstem tegmentum, cerebral periventricular white
matter, and cerebellar medulla. It is known to be prevalent in Japan and other Far Ease countries. The etiology of the acute necrotizing encephalopathy remains unknown. The typical course of acute necrotizing encephalopathy is the development of
the
irreversible neurologic symptoms related to brain lesions. The diagnosis can be made on the basis of the combination of a typical clinical profile and characteristic radiologic findings. We experienced a first case of acute necrotizing
encephalopathy in
a 9 month old boy in Korea. We report this case with the brief review of related literatures.
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Acute necrotizing encephalopathy; Thalamus; Brainstem tegmentum;
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