Dandy Walker ÁõÈıºÀÌ µ¿¹ÝµÈ Neurocutaneous Giant Melanosis 1·Ê
A Case of Neurocutaneous Giant Melanosis Associated with Dandy-Walker Syndrome
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È«¼ö¿µ/Su Young Hong
¹ÝÁöÀº/·ùÀçÈ£/ÃÖ¼ø¼·/Ȳ±Ô±Ù/Ji Eun Ban/Jae Ho Rhu/Sun Seob Choi/Kyu Geun Hwang
KMID : 0391520010090010171
Abstract
ÀúÀÚµéÀº 3¼¼ ³²¾Æ¿¡¼ Dandy-Walker ÁõÈıºÀÌ µ¿¹ÝµÈ neurocutaneous giant melanosis 1·Ê¸¦ °æÇèÇÏ¿´±â¿¡ ¹®Çå°íÂû°ú ÇÔ²² º¸°íÇÏ´Â ¹ÙÀÌ´Ù.
Neurocutaneous melanosis is a rate congenital phacomatosis, characterized by the presence of multiple pigmented skin nevi at birth. Meningeal melanosis tending to become malignant and seizure. Dandy-Walker syndrome is a developmental disorder of
brain
characterized by cystic dilatation of the fourth ventricle and agenesis of hypoplasia of the cerebellat vermis. We studied a case of Dandy-Walker syndrome with neurocutaneous giant melanosis in a 3 years old boy.
Å°¿öµå
Neurocutaneous giant melanosis; Dandy-Walker syndrome;
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