Immunoglobulin G4 비관련 특발성 경화성 장간막염
Immunoglobulin G4 Unrelated Idiopathic Mesenteric Sclerosis
권태형, 조광범, 이현직, 권선영, 이윤석,
소속 상세정보
권태형 ( Kwon Tae-Hyung )
계명대학교 의과대학 내과학교실
조광범 ( Cho Kwang-Bum )
계명대학교 의과대학 내과학교실
이현직 ( Lee Hyun-Jik )
계명대학교 의과대학 내과학교실
권선영 ( Kwon Sun-Young )
계명대학교 의과대학 병리학교실
이윤석 ( Lee Yoon-Suk )
인제대학교 의과대학 일산백병원 소화기내과
Abstract
Sclerosing mesenteritis is a rare benign disease with a prevalence of 0.16-3.4% and is characterized by chronic nonspecific inflammation and extensive fibrosis in the adipose tissue of the mesentery although the exact pathogenesis is still elusive. A 65-year-old woman was referred with suspicion of an abdominal mass and biliary stones on abdominal ultrasonography and CT. Bile duct stones were confirmed by endoscopic ultrasonography and successfully treated by endoscopic retrograde cholangiography with stone removal. Furthermore, a 4.7 cm conglomerated mass on small intestinal mesentery was suspected as sclerosing mesenteritis based on the features on abdominal MRI. However, because it could not be differentiated from malignancy without histologic examination, laparoscopic excisional biopsy was performed; it showed only inflammatory cells with extensive fibrosis. Therefore, the abdominal mass was confirmed as sclerosing fibrosis and the patient was followed-up without any treatments because no mass-related symptoms accompanied the findings. Six months later, abdominal CT showed no significant change in the mass. Herein, we report a rare case of incidentally found idiopathic sclerosing mesenteritis.
키워드
Sclerosing mesenteritis; Mesenteric panniculitis; IgG4-related disease
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