복막 암종증으로 진행한 자가면역성 췌장염 1예
Metachronous Development of Peritoneal Carcinomatosis in a Patient with Autoimmune Pancreatitis
이규원, 장재혁, 김진아, 김태호, 김창환, 김재광, 한석원,
소속 상세정보
이규원 ( Lee Kyu-Won )
Catholic University College of Medicine Department of Internal Medicine
장재혁 ( Chang Jae-Hyuck )
Catholic University College of Medicine Department of Internal Medicine
김진아 ( Kim Jean-A )
Catholic University College of Medicine Department of Pathology
김태호 ( Kim Tae-Ho )
Catholic University College of Medicine Department of Internal Medicine
김창환 ( Kim Chang-Whan )
Catholic University College of Medicine Department of Internal Medicine
김재광 ( Kim Jae-Kwang )
Catholic University College of Medicine Department of Internal Medicine
한석원 ( Han Sok-Won )
Catholic University College of Medicine Department of Internal Medicine
Abstract
Autoimmune pancreatitis (AIP) is a rare and unique type of chronic pancreatitis. The prognosis of AIP, particularly when associated with pancreatic cancer or a related malignancy, is not known. Only a few cases, where metachronous pancreas-related cancer developed during follow-up, have been reported. Most of these patients either underwent surgery or steroid therapy. This paper reports a case of a 66-year-old woman with untreated type I AIP who developed peritoneal carcinomatosis more than 2 years later. Initially, the patient had a markedly elevated serum IgG4 level and a diffuse, infiltrative mass-like lesion in the pancreatic head, in which the biopsy results were consistent with type I AIP. The patient was not treated with steroids because of a cerebellar infarction. Twenty-eight months after the diagnosis of AIP, peritoneal carcinomatosis developed without noticeable changes in the pancreas from the initial findings.
키워드
Autoimmune pancreatitis; Immunoglobulin G4-related disease; Pancreatic neoplasms; Peritoneal neoplasms
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