자가면역간염과 원발성 경화담관염을 가진 중복증후군 소아 환자에서 발생한 형질세포성 골수염 1예
A Case of Chronic Lymphoplamacellular Osteomyelitis with Autoimmune Hepatitis/Primary Sclerosing Cholangitis Overlap Syndrome in a Child
이지혁, 이현영, 최연호, 김진규, 이지현,
소속 상세정보
이지혁 ( Lee Ji-Hyuk )
성균관대학교 의과대학 삼성서울병원 성형외과학교실
이현영 ( Lee Hyun-Young )
성균의대 삼성서울병원 소아과학교실
최연호 ( Choe Yon-Ho )
성균관대학교 의과대학 삼성서울병원 소아과학교실
김진규 ( Kim Jin-Kyu )
성균관대학교 의과대학 삼성서울병원 소아과학교실
이지현 ( Lee Jee-Hyun )
성균관대학교 의과대학 삼성서울병원 소아과학교실
KMID : 0816120070100010091
Abstract
The Overlap syndrome is characterized by a combination of the major hepatobiliary autoimmune diseases such as autoimmune hepatitis, primary biliary cirrhosis and primary sclerosing cholangitis. It is frequently accompanied by inflammatory bowel disease. Chronic lymphoplasmacellular osteomyelitis is characterized by recurrent episodes of bacterial osteomyelitis and is associated with autoimmune diseases (especially inflammatory bowel disease). We report the case of a girl who was diagnosed with ulcerative colitis and autoimmune hepatitis at 4 years of age and with the overlap syndrome with primary sclerosing cholangitis at 6 years. At 9 years, she was diagnosed with chronic lymphoplasmacellular osteomyelitis.
키워드
Overlap syndrome;Autoimmune hepatitis;Primary sclerosing cholangitis;Chronic lymphoplamacellular osteomyelitis
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