전기진단검사상 축삭 병변을 보인 밀러 피셔 증후군 1예
A Case of Miller Fisher Syndrome Showing Axonal Polyneuropathy in Electrodiagnostic Test
손민균, 김봉옥, 전경진, 김상수,
소속 상세정보
손민균 ( Sohn Min-Kyun )
충남대학교 의과대학 재활의학교실
김봉옥 ( Kim Bong-Ok )
충남대학교 의과대학 재활의학교실
전경진 ( Jun Kyung-Jin )
충남대학교 의과대학 재활의학교실
김상수 ( Kim Sang-Soo )
충남대학교 의과대학 재활의학교실
KMID : 0860920040060010067
Abstract
Miller Fisher syndrome is clinically characterized by the triad of gait ataxia, external ophthalmoplegia and areflexia. A six-tear-old girl developwd ophthalmoplegia and mydriasis after a febrile flu-like illness. She had additional symptoms of dysphgia, bulbar palsy, ataxia, areflexia and weakness of extrrmities. She was unable to maintain an upright posture, nor able showed mild albimino-cytologic dissociation and electrodiagnostix study revealed a predominantly motor axonal peripheral polyneuropathy including both facial nerves. She was placed on a high dose of intravenous immunoglobulin and comprehensive rehavilitation treatment which resulted on a complete recovery in 6 month. This is a case of Miller Fisher syndrom which presented atypically severe weakness of extremities in clinically and generalized motor axnal polyneuropathy in electrodiagnodtically.
키워드
Miller Fisher Syndrome;Total ophthalmoplegia;Axonal Neutopathy
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