다발성 뇌엽 피질절제술에 의한 소아 Sturge-Weber Syndrome의 외과적 치험 1례 -증례보고-
A Case of Pediatric Patient with Sturge-Weber Syndrome Treated Surgically Using a Multiple Lobar Corticectomy -Case Report-
이관성, 전신수, 강준기, 김영인,
소속 상세정보
이관성 ( Lee Kwan-Sung )
가톨릭대학교 의과대학 강남성모병원 신경외과
전신수 ( Jeun Sin-Soo )
가톨릭대학교 의과대학 강남성모병원 신경외과
강준기 ( Kang Joon-Ki )
가톨릭대학교 의과대학 신경외과학교실
김영인 ( Kim Yeong-In )
가톨릭대학교 의과대학 신경과학교실
KMID : 0877219980020020154
Abstract
Seizures are the major neurological features of Sturge-Weber Syndrome (SWS) and mostly become intractable. After the onset of uncontrollable seizures, patients may develop a progressive hemiparesis, hemianopsia and mentally retarded. Surgery is recommended as early as possible lo ensure maximal recovery. We report a pediatric case of SWS who was treated surgically. Unlike the routinely performed hemispherectomy procedures, the patient underwent a limited multiple lobar corticectomy because the patient demonstrated mild hemiparesis and preservation of digital dexterity on the affected hand at the time of operation pathology. The pathology showed typical features of SWS With respect to control of intractable seizures, good surgical result was achieved without resecting the whole heimsphere.
키워드
스터지-웨버증후군; 간질 다발성 뇌엽 피질 절제술
Sturge-Weber syndrome; Seizure; Multiple lobar corticectomy
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