결절성 경화증에서 나타난 홍소발작 1례
Gelastic Seizures in a Patient with Tuberous Sclerosis
김성희, 김광수, 민지원, 유봉구, 유경무,
소속 상세정보
김성희 ( Kim Seong-Hee )
고신대학교 의과대학 신경과학교실
김광수 ( Kim Kwang-Soo )
고신대학교 의과대학 신경과학교실
민지원 ( Min Ji-Won )
고신대학교 의과대학 신경과학교실
유봉구 ( Yoo Bong-Goo )
고신대학교 의과대학 신경과학교실
유경무 ( Yoo Kyung-Moo )
고신대학교 의과대학 신경과학교실
KMID : 0877220020060020150
Abstract
Background: Gelastic seizures are characterized by ictal inappropriate sudden laughter as the predominant seizure manifestation. they are very rare and may occur in patients with hypothalamic hamartomas, pituitary tumors, astrocytomas of the mamillary bodies, CNS infection, trauma, and dysraphic condition.
Case: A 21-year-old woman with tuberous sclerosis was admitted due to frequent sudden inappropriate laughter as a seizure manifestation. EEG showed paroxysmal brief generalized 4-5 Hz spike and wave complexes. Brain MRI revealed multiple tubers in the bilateral cerebral cortical areas, right caudate nucleus, and left anterior cingulate gyrus. We tried vigabatrin, but gelastic seizures were not controlled.
Comment:We report a case of gelastic seizures associated with tuberous sclerosis, which has not previously been reported in Korea.
키워드
Gelastic seizures; Tuberous sclerosis
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