Moyamoya Disease Presenting as Transient Amnesia with Cortical Blindness
홍준영, 나상준, 신정원, 김현숙, 김원찬, 김옥준, 오승헌, 이기욱,
소속 상세정보
홍준영 ( Hong Jun-Yeong )
Konyang University College of Medicine Department of Neurology
나상준 ( Na Sang-Jun )
Department of Anesthesiology and Pain Medicine, Konyang University College of Medicine Daejeon, Korea
신정원 ( Shin Jung-Won )
CHA University CHA Bundang Medical Center Department of Neurology
김현숙 ( Kim Hyun-Sook )
CHA University CHA Bundang Medical Center Department of Neurology
김원찬 ( Kim Won-Chan )
CHA University CHA Bundang Medical Center Department of Neurology
김옥준 ( Kim Ok-Joon )
CHA University CHA Bundang Medical Center Department of Neurology
오승헌 ( Oh Seung-Hun )
CHA University CHA Bundang Medical Center Department of Neurology
이기욱 ( Lee Kee-Ook )
CHA University CHA Bundang Medical Center Department of Neurology
Abstract
Symptoms of moyamoya disease (MMD) are typically associated with regions of the brain supplied by the internal carotid arteries and middle cerebral arteries. We describe a patient who presented with transient cortical blindness, anosognosia, and amnesia associated with MMD. A 22-year-old right-handed woman presented with amnesia and visual impairments. She completely denied blindness and recent memory disturbances with confabulation. Diffusion and T2-weighted magnetic resonance imaging showed high signal intensities on the left basal ganglia, suggesting an acute ischemic stroke. In cerebral angiography, complete occlusion of the distal internal carotid artery was shown, with collateral flow noted within the posterior cerebral artery. Neuropsychological and cognitive problems related to MMD have been previously reported in the literature. We believe that these symptoms reflect transient ischemia caused by a disturbed hemodynamic status. This case report demonstrates that patients with MMD can present with transient posterior circulation symptoms in the form of Dide-Botcazo syndrome.
키워드
Moyamoya disease; Blindness, Cortical; Amnesia; Cerebral infarction
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