A Rare Case of Small Bowel Undifferentiated Pleomorphic Sarcoma: Imaging Findings on CT and Magnetic Resonance Enterography
한여은, 채수영, 이정현, 박범진, 성득제, 한나연, 심기춘, 김민주,
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한여은 ( Han Yeo-Eun )
Korea University College of Medicine Korea University Anam Hospital Department of Radiology
채수영 ( Chae Soo-Young )
Korea University College of Medicine Korea University Anam Hospital Department of Radiology
이정현 ( Lee Jeong-Hyeon )
Korea University College of Medicine Korea University Anam Hospital Department of Pathology
박범진 ( Park Beom-Jin )
Korea University College of Medicine Korea University Anam Hospital Department of Radiology
성득제 ( Sung Deuk-Jae )
Korea University College of Medicine Korea University Anam Hospital Department of Radiology
한나연 ( Han Na-Yeon )
Korea University College of Medicine Korea University Anam Hospital Department of Radiology
심기춘 ( Sim Ki-Choon )
Korea University College of Medicine Korea University Anam Hospital Department of Radiology
김민주 ( Kim Min-Ju )
Korea University College of Medicine Korea University Anam Hospital Department of Radiology
Abstract
Gastrointestinal tract involvement in undifferentiated pleomorphic sarcoma (UPS) is extremely rare. To the authors' knowledge, only 21 cases of primary small bowel UPS have been reported in the literature available in English. Reported CT findings in primary small bowel UPS have been nonspecific, and MRI findings have been reported in only one case. The present article describes a case involving a 72-year-old male with histologically confirmed primary UPS arising from the ileum, focusing on both CT and magnetic resonance enterography findings. On CT, primary small bowel UPS was noted as a heterogeneously enhanced small bowel mass without obstruction. Magnetic resonance enterography revealed heterogeneous intermediate T1 and T2 signal intensity, with hemorrhagic or necrotic foci within the mass and heterogeneous enhancement. The differential diagnosis included malignant gastrointestinal tumor; however, the prognosis of UPS is worse, with higher incidences of extra-abdominal metastasis.
키워드
Malignant Fibrous Histiocytoma; Histiocytoma; Pleomorphic Malignant Fibrous Histiocytoma; Small Intestine; Tomography, X-Ray Computed; Magnetic Resonance Imaging
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