재발성 항문주위 Paget씨병 1예
A Case of Recurrent Perianal Paget’s Disease
박상영, 강원경, 박종경, 김지연, 박승철, 안창혁, 오승택,
소속 상세정보
박상영 ( Park Sang-Young )
경상대학교 의학전문대학원 피부과학교실
강원경 ( Kang Won-Kyung )
가톨릭대학교 의과대학 외과학교실
박종경 ( Park Jong-Kyung )
가톨릭대학교 의과대학 외과학교실
김지연 ( Kim Ji-Youn )
가톨릭대학교 의과대학 외과학교실
박승철 ( Park Seung-Cheol )
가톨릭대학교 의과대학 외과학교실
안창혁 ( An Chang-Hyeok )
가톨릭대학교 의과대학 외과학교실
오승택 ( Oh Seung-Tack )
가톨릭대학교 의과대학 외과학교실
KMID : 0356720010170060346
Abstract
Extramammary Paget’s disease is an uncommon intraepithelial carcinoma of the skin and mucosa usually occurring in the anogenital area. Perianal Paget’s disease is a rare entity, often associated with internal malignancies and a poor prognosis. Clinical manifestations of perianal Paget’s disease include pruritis (most common), irritation, rash, lump sensation and the lesion shows erythematous, crusted or scaly area which may weep clear fluid. Lichenified, leukokeratotic or leukoplakia-like patches may also develop in some patients. These areas may resemble eczema or contact dermatitis. Many authors recommend surgery as the treatment of choice. Extended surgical excision for non-invasive lesion and excision of rectum or abdominoperineal resection for invasive disease is recommended. The prognosis for non-invasive lesion is excellent, but for invasive lesion is poor. We experienced one case of perianal Paget’s disease which recurred after wide excision of vulvar area for Paget’s disease, and performed secondary abdominoperineal resection. Now, radiation therapy was done for adjuvant therapeutic modality.
키워드
Paget씨병;재발성;항문
Paget’s disease;Recurrent;Anus
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