Potter 증후군 - 1부검 증례 보고 -
Potter's Syndrome -An autopsy case report-
소속 상세정보
윤혜경/Hye Kyoung Yoon
주종은/석동수/Jong Eun Joo/Dong Soo Suk
KMID : 0357919850190010125
Abstract
Potter's syndrome was originally described as combination of bilateral renal agenesis
and unique progeric facial characteristics in 1946 by Potter. In cases of severe renal
maldevelopment such as bilateral polycystic kidney or marked hypoplasia, similar facial
features has been also associated.
At 1963, Potter and Osathanondth reported classification of polycystic kidney as Type
I-Ⅳ by microdissection study.
Recently authors experienced an autopsy case of polycystic kidney with characteristic
potter face, and other combined malformations such as ; absence of both ureters and
urinary bladder, pulmonary hypoplasia, undescended testes and oligo-hydramnios, fetal
growth retardation and breech presentation. According to the classification of polycystic
kidney of Potter and Osathanondth, this presenting case is compatible with type Ⅱ
B.
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